Wiskott-Aldrich chirwere

Zvemukati

• Zviratidzo zveWiskott-Aldrich Syndrome
• Kurapa kweWiskott-Aldrich Syndrome

Wiskott-Aldrich syndrome chirwere chemajini, chinokanganisa immune system inosanganisira T neB B lymphocyte, uye masero eropa anobatsira kudzora kubuda ropa, maplatelet.

Zviratidzo zveWiskott-Aldrich Syndrome

Zviratidzo zve wiskott-Aldrich syndrome inogona kuva:

Tsika yekubuda ropa:

• Yakaderedzwa nhamba uye saizi yemaplatelet muropa;
• Kucheka kweropa kunocheka kunoratidzwa nemavara matsvuku-ebhuruu saizi yemusoro wepini, unonzi "petechiae", kana iwo angave akakura uye akafanana nemavanga;
• Zvituru zvine ropa (kunyanya muhucheche), kubuda ropa matadza uye kubuda kwenguva refu kwemhino dzemhino.

Kazhinji hutachiona hunokonzerwa nemhando dzese dzehutachiona senge:

• Otitis media, sinusitis, mabayo;
• Meningitis, mabayo anokonzerwa nePneumocystis jiroveci;
• Utachiona hwehutachiona hwehutachiona hunokonzerwa nemolluscum contagiosum.

Eczema:

• Kakawanda zvirwere zveganda;
• Nzvimbo dzakasviba paganda.

Autoimmune kuratidzwa:

• Vasculitis;
• Hemolytic kupererwa neropa;
• Idiopathic thrombocytopenic purpura.

Kuongororwa kwechirwere ichi kunogona kuitwa nachiremba wevana mushure mekucherechedzwa kwechipatara kwezviratidzo uye nemimwe miedzo. Kuongorora saizi yemaplatelet ndiyo imwe yenzira dzekuongorora chirwere ichi, sezvo hosha shoma dziine hunhu uhu.

Kurapa kweWiskott-Aldrich Syndrome

Mushonga wakakodzera kwazvo weWiskott-Aldrich syndrome ndeyekutsvaira kwemongo wemapfupa. Dzimwe nzira dzekurapa kubviswa kwepleen, sezvo nhengo iyi ichiparadza maplatelet mashoma ane vanhu vane chirwere ichi, kuiswa kwehemoglobin uye kushandiswa kwemishonga inorwisa mabhakitiriya.

Hupenyu hunotarisirwa kune vanhu vane chirwere ichi hwakaderera, avo vanopona mushure memakore gumi vanowanzo kuve nemamota akadai se lymphoma uye leukemia.