Munyori: Mark Sanchez
Zuva Rekusika: 27 Ndira 2021
Gadziridza Zuva: 1 Kubvumbi 2025
Anonim
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Porphobilinogen (PBG) ndeimwe yemhando dzinoverengeka dze porphyrins dzinowanikwa mumuviri wako. Porphyrins anobatsira kuumba zvinhu zvakawanda zvakakosha mumuviri. Imwe yeiyi hemoglobin, puroteni iri mumasero matsvuku eropa anotakura oxygen muropa. Porphyrins anowanzo siya muviri wako kuburikidza neweti kana zvituru. Kana izvi zvikasaitika, porphyrins dzakadai sePBG dzinogona kuvaka mumuviri wako.

Ichi chinyorwa chinotsanangura bvunzo kuyera huwandu hwePBG mune weti sampuro.

Mushure mekupa iwe weti sampuro, inoedzwa murabhor. Izvi zvinonzi zvisina kujairika weti sampuro.

Kana zvichidikanwa, mupi wako wezvehutano anogona kukukumbira kuti utore weti yako kumba kwemaawa anopfuura makumi maviri nemana. Iyi inonzi 24-awa weti sampuro. Wako mupi achakutaurira maitiro ekuita izvi. Tevera mirairo chaizvo.

Mupi wako anogona kukuudza kuti umbomira kutora mishonga inogona kukanganisa mhedzisiro yekuedzwa. Ive neshuwa yekuudza mupi wako nezveese mishonga yaunotora. Izvi zvinosanganisira:

  • Mishonga inorwisa mabhakitiriya uye anti-fungal zvinodhaka
  • Anti-kunetseka zvinodhaka
  • Mapiritsi ekudzivirira kubata pamuviri
  • Chirwere cheshuga
  • Mishonga yemarwadzo
  • Kurara mishonga

Usamborega kutora chero mushonga usati watanga kutaura kune wako mupi.


Uyu muedzo unosanganisira chete zvakajairwa kuita weti, uye hapana kusagadzikana.

Uyu muedzo unogona kuitwa kana mupi wako achifungidzira porphyria kana chimwe chirwere chinosangana neisina kujairika PBG nhanho.

Kune yakasarudzika weti sampuro, isina kunaka bvunzo mhedzisiro inoonekwa seyakajairika.

Kana iyo bvunzo ikaitwa pane 24-awa weti sampuro, iyo yakajairika kukosha iri pasi pemamirigiramu mana paawa makumi maviri nemana (18 micromoles pamaawa makumi maviri nemana)

Zvakajairika kukosha masenduru anogona kusiyana zvishoma pakati pemarabhoritari akasiyana. Mamwe marabhoritari anoshandisa zviyero zvakasiyana kana anogona kuyedza mhando dzakasiyana. Taura nemupi wako nezve zvinorehwa nemimwe miedzo yako.

Iyo yakawedzera nhanho yePBG mune weti inogona kunge iri nekuda kwe:

  • Hepatitis
  • Kutungamira muchetura
  • Kenza yechiropa
  • Porphyria (akati wandei mhando)

Iko hakuna njodzi nemuedzo uyu.

Porphobilinogen bvunzo; Porphyria - weti; PBG

  • Urume urinary system

Yakazara SJ, Wiley JS. Heme biosynthesis uye kusagadzikana kwayo: porphyrias uye sideroblastic anemias. Muna: Hoffman R, Benz EJ, Silberstein LE, et al, eds. Hematology: Basic Misimboti uye Maitiro. 7th ed. Philadelphia, PA: Elsevier; 2018: chitsiko 38.


Riley RS, McPherson RA. Yekutanga kuongorora weti. Mune: McPherson RA, Pincus MR, eds. Henry's Clinical Diagnosis uye Management nemaLabhoritari Maitiro. 23rd ed. St Louis, MO: Elsevier; 2017: chitsiko 28.

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